Kiwon lafiya, Cututtuka da kuma Yanayi
Gilbert ta ciwo: da mafi m, a matsayin bi, da forecast
Gilbert ta ciwo - wani hereditary cuta, wadda aka ruwaito daga rinjaye kwayoyin halittu na daya iyaye da kuma pigment ne steatosis. An halin akai karuwa a Sakakken bilirubin cuta da kuma safarar shi zuwa hepatocytes. "Gilbert ta ciwo" domin sauki mazauni ba zai ce wani abu magana. Ta yaya hatsari irin wannan ganewar asali? Bari mu dubi tare.
epidemiology
Bugu da kari, shi ne kai tsaye alaka jima'i da shekaru. The matasa da shekaru da alama na zanga-zangar a sau da yawa ne ya fi a manya. Game da sau goma fiye da kowa a cikin maza.
pathogenesis
A cuta ne take hakkin bilirubin su safarar wasu gabbansa hepatocytes domin ta dauri da glucuronic acid. A dalilin - Pathology na cell bango na kai tsarin, kazalika da wani enzyme da ta ɗaure bilirubin tare da sauran abubuwa. All tare da shi qara abun ciki na bukatuwa izuwa bilirubin a cikin jini. Kuma tun yana da matuƙar narkewa a cikin fats, duk da kyallen takarda, Kwayoyin dake dauke da lipids, tara shi, ciki har da kwakwalwa.
Akwai a kalla biyu siffofin da ciwo. A farko faruwa a kan bango na canzawa erythrocytes, da kuma na biyu na inganta su hemolysis. Bilirubin da Gilbert ta ciwo ne mafi traumatic wakili cewa halaka jikin mutum. Amma ya aikata shi sannu a hankali don haka da cewa shi ba ya jin har zuwa wani lokaci.
asibitin
Neurological cututtuka ne da rauni, juwa ko jiri, gajiya. Zai yiwu rashin barci ko barci cuta a cikin nau'i na mafarki. Ko da more wuya, wani ciwo da halin bayyanar cututtuka na dyspepsia Gilbert:
- m iyawa a bakin.
- belching.
- ƙwannafi.
- takaici da kujera.
- tashin zuciya da kuma amai.
m dalilai
bincikowa da
Yana duk farawa da anamnesis. Likita ya tambaye probing tambayoyi:
- Mene ne gunaguni?
- Har yaushe suka wuce akwai sha raɗaɗin a dama babba quadrant da kuma abin da suke?
- Shin, akwai wani hanta cuta a cikin dangi?
- ko haƙuri lura da duhun fitsari? Idan haka ne, abin da yake da shi ta ɗaure?
- Abin da abinci da bãyukansu?
- Shin da magani? Shin, ba su taimake shi?
Sa'an nan ya zo da jarrabawa. Kula da jaundiced fata da kuma sclera, zafi a lokacin palpation na ciki. Bayan jiki hanyoyin zo da nuna of dakin gwaje-gwaje gwaje-gwaje. Test "Gilbert ciwo" bai yi ba tukuna ƙirƙira shi, don haka abin da likitoci da kuma janar likitoci an iyakance ga daidaitattun bincike yarjejeniya.
Yana hada dole cikakken jini count (halin da ya karu haemoglobin, gaban m siffofin da maikacin jini). Next zo da Biochemistry na jini baya gare shi, wanda an riga an tura assesses jihar na jini. Bilirubin aka ƙara a kananan adadin hanta m lokaci sunadaran enzymes kuma ba su pathognomonic alama.
A lokuta da cutar hanta da marasa lafiya, ku aikata dukan coagulation to daidaita krovosvertyvayuschee iya aiki idan ya cancanta. Abin farin, tare da Gilbert ta ciwo munanan qananan.
Musamman dakin gwaje-gwaje gwaje-gwaje
Manufa bincike zaɓi ne don nazarin kwayoyin DNA da PCR takamaiman genes da suke da alhakin musayar bilirubin Irinta. Don ware hepatitis kamar yadda Sanadin cutar hanta, ba serological martani ga antibodies to wadannan ƙwayoyin cuta.
Na janar nazarin compulsorily ciyar more urinalysis. Kimanta ta launi, tsabta, yawa, kasancewa na salon salula abubuwa da kuma pathological impurities.
Bugu da kari, yin takamaiman bincike gwaje-gwaje domin karin sosai rajistan shiga na bilirubin. Suna da dama iri:
- Test da yunwa. An sani cewa bayan kwanaki biyu na kalori ƙuntatawa a cikin mutane da matakin da wannan enzyme ne ta ƙara da rabi zuwa biyu sau. Ya isa ya dauki analysis a baseline, sa'an nan 48 hours daga baya.
- Nicotine gwajin. A haƙuri aka intravenously gudanar zuwa arba'in milligrams na nicotinic acid. Yana kuma ana sa ran wata karuwa a bilirubin matakan.
- Barbiturate gwajin: samun phenobarbital uku milligrams da kilogram kwanaki biyar, haifar da wani m ƙi a cikin enzyme matakin.
- Rifampitsinovaya samfurin. Kawai shiga tara milligrams na kwayoyin ƙara da matakin na bukatuwa izuwa bilirubin.
instrumental nazarin
Na farko shi ne, ba shakka, da Amurka. Tare da shi, za ka iya ganin tsarin da kuma jinin samar ba kawai hanta da kuma biliary tsarin, amma kuma sauran kogon ciki su hana su Pathology.
Sa'an nan ya zo da kwamfuta scanning. Sake, to ware duk sauran m diagnoses, tun Gilbert ta ciwo hanta tsarin zauna canzawa.
A mataki na gaba - a biopsy. Yana gusar marurai metastasis damar domin kara biochemical da kwayoyin da bincike tare da wani samfuri na nama da kuma sa karshe ganewar asali. A madadin ne elastography. Wannan hanya damar tantance mataki na degeneration na connective nama da kuma hanta fibrosis a share.
yara
Gilbert ta ciwo a yara bayyana kanta a uku zuwa goma sha uku shekaru. A ingancin da tsawon rai, ya ba ya canzawa, don haka gagarumin canje-canje a cikin yaro ta ci gaba ba da taimako. Tsokane ta bayyana a cikin yara zai iya jaddada, jiki aiki, farkon haila a 'yan mata da kuma balaga a boys, likita shiga tsakani a cikin nau'i na aiki.
Bugu da kari, kullum cututtuka, zazzabi for fiye da kwana uku, hepatitis A, B, C, E, da kuma Ari Ari turawa jiki matsalar aiki na samfur.
Rashin lafiya da kuma aikin soja
The saurayi ko matashi kamu - Gilbert ta ciwo. "Ka ɗauki idan sojojin tare da wannan cuta?" - kawai tunanin mahaifansa biyu, kuma shi da kansa. Bayan duk, tare da wannan cuta bukatar a hankali magance jikinka, da kuma soja a kowace hanya don wannan ba shi da.
Bisa ga tsari na ma'aikatar tsaron kasar, matasa maza daga Gilbert ta ciwo suna kira ga soja, amma yana da wasu reservations game da wurin da sharuddan da yanayi. Gaba daya kubuce conscription za su ci nasara ba. Domin jin kyau, kana bukatar ka bi wadannan sauki sharudda:
- Kada ka sha barasa.
- To kuma ci dama.
- Kauce wa m motsa jiki.
- Kada ku riƙi kwayoyi, adversely shafi cikin hanta.
Saboda haka conscripts manufa domin aikin a hedkwatar, misali. Duk da haka, idan ka so qwarai da ra'ayin zama soja, sa'an nan daga shi zai yi ba, kamar yadda Gilbert ta ciwo da kuma sana'a sojojin - ne m. Riga lokacin da ake ji wa mafi girma ilimi a kan daidai profile hukumar za a tilasta su da su kãfirta da su saboda wasu dalilai.
Saboda haka abin da idan ka, ko kuma ka iyali da aka kamu da Gilbert ta ciwo, "Ka ɗauki akwai sojoji?" - shi ne babu mafi gaggawa tambaya.
magani
Abu na biyu, daga cikin mutum da ake bukata domin cika da barci da kuma sauran, ba za a load kanka jiki wuya, kada dauki kwayoyi ba tare da tuntubar likita. A matsayin tushen rai-style ya kamata a zabi guje cutarwa halaye, kamar yadda nicotine da barasa halakar da ja da maikacin jini, da kuma wannan yana rinjayar da adadin free bilirubin a cikin jini.
Idan duk abin da aka yi amfani da daidai, shi ya sa shi kusan unnoticeable Gilbert ta ciwo. Ta yaya hatsari da komowa ko gazawar na rage cin abinci? A kalla bayyanar jaundice da kuma sauran m sakamakon. Lokacin da manifestirovanii cututtuka rubũta barbiturates, cholagogue da gepatoprotektory. Bugu da ƙari kuma, suka ɗauke prophylaxis na gallstone samuwar. amfani chelators, UV radiation da enzymes don taimakon narkewa don rage bilirubin matakin.
rikitarwa
Matsayin mai mulkin, kada ku damu da wannan ba wani hereditary cuta. Dako na da dogon-rayu, kuma suna dauke da fitar da likita ya umarta, sa'an nan da farin ciki. Duk da haka, wani mulki akwai ban. Saboda haka, abin da surprises iya bayar da Gilbert ta ciwo? Ta yaya kawo hadari ne jinkirin amma tabbatar da gazawar da compensatory yiwuwa na jikin mutum?
A mafi munin laifi gwamnatin Syria da kuma rage cin abinci zai ƙarshe ci gaba kullum hepatitis, da kuma warkar da shi ne ba zai yiwu. Wajibi ne a yi da hanta dashi. Wani m matsananci - cholelithiasis, wanda kuma ba ya bayyana kanta ga wani dogon lokaci, sa'an nan kuma haddasa wata da karfi duka zuwa ga jiki.
rigakafin
Ga wani ya, Gilbert ta ciwo. Mẽne ne, da sauki amsar ne har yanzu da wuya kalmomi. Matakai a cikin jiki ne ma rudani zuwa gare su a lokaci daya fahimta da kuma yarda da.
Abin farin, mutane da wannan cuta da wani dalilin tsõron su nan gaba. Musamman hypochondriac mutum zai iya wani malaise dangana ga Gilbert ta ciwo. Ta yaya kawo hadari ne wannan m? Overdiagnosis duk a lokaci daya.
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