Cututtukan Wilson-Konovalov: Sanadin cutar, Cutar cututtuka da jiyya

Abincin Wilson-Konovalov shine cututtukan da ke haifar da ƙananan ƙarfin jan ƙarfe a cikin jiki saboda jinkirtacciyar jinkiri da rashin kuskure kuma sakamakon sakamakonsa a cikin takarda da gabobin ciki (a cikin hanta, fatalwar ido, kodan, kwakwalwa). Sanadin cutar

Wannan cutar ta haifar da kwayoyin halitta. Abincin Wilson-Konovalov a cikin zuciya na bayyanar ta asibiti shine cin zarafin matakai na musanya. A cikin jiki na al'ada, mafi yawan wannan nau'in sinadaran, a cikin jini daga hanji, an cire shi a cikin fitsari da kuma bile. Cutar Wilson-Konovalov tana haifar da cin zarafi na tsarin da ake amfani da shi na jan ƙarfe a cikin hanta (kira na ceruloplasmin-furotin dake daura da jan karfe) da kuma raguwa da shi tare da bile. A sakamakon haka, matakin jan ƙarfe mai tsabta yana ƙaruwa cikin jini.

Wilson ta cuta da aka gada daga kakanni autosomal recessive hanya. Yawan yawan cututtuka yafi girma a ƙasashe da yankuna inda aka yarda da aure tsakanin dangi. Maganin maganganun cutar wannan cuta ya wuce 60%. Akwai nau'o'i uku na kwayar cuta:

• West. Farawa cikin shekaru 10-16 tare da ciwon hanta. Sa'an nan kuma akwai wata alama ta ilimin lissafi.
• Slavic. Fara, a matsayin mai mulkin, a shekaru 20-35. A wannan yanayin, an lura da ƙananan ƙananan ciwon hanta da kuma alamun kwaikwayo neurological.
• Atypical. Ana nuna shi ta hanyar ragewa a matakin cerulplasmine. Clinical ãyõyin cuta ana kiyaye.

Sakamakon ƙarfin jita-jita a wasu ɓangarori na ciki

Haɗuwa da jan karfe a cikin kodan zai haifar da ci gaban glomerulonephritis kuma saboda sakamakon cin zarafi na filtration na sunadaran da ions. Sakamakon haka shine haɗari mai yawa daga jiki tare da fitsari. Lokacin da jan accumulates a cikin cornea na ido, ba zai shafi motility na eyeball, kuma ba ya haifar da na gani hanawa, duk da haka, yana sa wani canji a cikin launi da'ira a cikin Iris. Wannan yana daya daga cikin siffofin halayen wanda cutar Wilson-Konovalov ta sauƙaƙe. Hotunan da ake nuna launin launin rawaya a kan idanu ga ido mara kyau, magana don kansu. Copper, tara a cikin kwakwalwa, take kaiwa ga bayyanar jerin sifofi na cututtuka. Hada shi a cikin hanta yana haddasa lalacewar wannan kwayar, wanda zai haifar da ketare ayyukansa, ya kara yawan maye cikin jiki da kuma cirrhosis.

Abincin Wilson-Konovalov: bayyanar cututtuka

Sakamakon farko na wannan cuta zai iya zama magana mai lalacewa da wahalar yin kananan ƙungiyoyi. Akwai kuma rawar jiki da kai da ƙananan ƙwayoyi a lokacin motsa jiki da kuma sauran hutawa, har da tsayayyar tsokoki da ƙungiyoyi. Haka kuma cutar ta ci gaba da cigaba, tare da yin musanyawa da gafara. A mutuwa sakamako ne mafi akai-akai lura a yara tare da hanta nau'i na cutar.

Jiyya

Yin maganin wannan cuta yana amfani da kwayoyi da suke daidaita ka'idar jan karfe a jiki. An tsara su ne kawai a kan kowane mutum, dangane da nau'in da kuma aikin cutar. Ana haɓaka kayan ado a lokaci daya tare da kula da jan karfe cikin jini. Wadannan kwayoyi suna dauke da karfi da jiki kuma suna da tasiri mai karfi, don haka tare da su suna wajabta haɓaka ma'adanai da bitamin. Marasa lafiya rika tsaya ga rage cin abinci, wanda zame daga cikin abinci abinci mai arziki a cikin jan (kifi, cakulan, namomin kaza, hanta, koko).