Alamun da kuma lura da Landau-Kleffner ciwo

Landau-Kleffner ciwo - An samu farfadiya aphasia a yara. An halin take hakkin magana aiki. A wannan yanayin, sha ba da bayani aka gyara na magana (sauti canji ta hanyar da hakora, da harshe, da kuma makogwaro), da kuma ikon m da phoneme a tsakiya m tsarin matakin. Af, shi ne a wasu wurare a cikin cerebral bawo.

A cuta ya auku a gaba daya lafiya yara. Farko da suka rasa da ikon daidaita zuwa waje muhalli, sa'an nan ba zai iya zama ma'ana, a fili da kuma Azancin ra'ayinsu. Gaskiyar cewa a cikin kwakwalwa na baby ne pathological canje-canje, ya nuna EEG. A ciwo aka bayyana a cikin shekarar 1957 ta biyu masana kimiyya - Landau Kleffner. Saboda haka, su sunayen da kira wannan cuta.

A Sanadin cutar

Sanadin Landau-Kleffner ciwo ba da cikakken bayyana. Ko da yake a wasu lokuta, likitoci za su iya gane wani factor da ya kai ga ci gaban da cutar. A farko wuri - shi ne cikin rufaffiyar shugaban rauni, kwakwalwa ƙari, wata parasitic cuta sa da larvae na naman alade tapeworm - neurocysticercosis. A dalilin iya zama, kuma autoimmune demyelinating cututtuka, a cikin abin da akwai halakar da fari al'amari na cikin juyayi tsarin - myelin. Fararwa da ci gaban da ciwo ne kuma m kumburi a cikin jirgin ruwa bango a yankin na kwakwalwa. Mahara aukuwar cututtuka da aka hade da wani rashi na mitochondrial numfashi hadaddun. Wani lokaci cikin hanyar zama ma na bakin ciki bawo, sakamakon da yaro tasowa da abin ya shafa yammancin duniya.

A ciwo iya zama fulminant form. Wannan shi ne jiya wani biyu-shekara Toddler tafiya, magana, kuma ya kasance daidai da lafiya yaro, kuma a yanzu ya farka, iya daura, da kuma 'yan kalmomi. Wani lokaci, cutar progresses sannu a hankali, marmashi hankali hasarar da ikon fi'ili sadarwar da isasshen ji na gaskiya.

Mene ne bayyanar cututtuka?

mace masanin kimiyya cutar da aka bayyana a cikin daki-daki, Alexandrov N. Sh Landau-Kleffner ciwo, ta ce, akwai kuma saboda abin da ake kira kwakwalwa plasticity. Shi ne kamar yadda idan "restructured" ga mafi alhẽri yi su ayyuka. A kan aiwatar da wannan canji da kuma tasowa a wucin gadi aphasia. Kamar yadda shi ne yanayin da ya samu tsari, raunin da ya faru da cututtuka da lalacewa ta hanyar irin wannan Pathology za a iya bincikar lafiya ta amfani da EEG. Bugu da kari, "na farko kararrawa" na iya zama farfadiya seizures, abin da ya bayyana a yaro. Su ne a 70% na lokuta tare da farko na cutar.

Around kwata na duk lokuta, da haƙuri hasarar magana aiki ga wata. Amma mafi yawan asarar faruwa kusan instantaneously. Wani lokaci a jariri ba zai iya furta sauti. Rabin da marasa lafiya gani halayya cuta. Aiki tunani ne kiyaye. Tare da shekaru, da seizures bace. Cikakken ko m dawo da jawabin ayyuka faruwa ga shekaru 16.

tabarbarewar magana

Landau-Kleffner ciwo a wani yaro zai fara da asarar da aiki na jawabin - wannan shi ne daya daga cikin babban bayyanar cututtuka da cutar. An halin fi'ili ko auditory agnosia - sosai ji, wanda adana sani da kuma ji na ƙwarai. A cikin farko idan, haƙuri shi ne kasa yin magana da kyau. A karo na biyu - ya ba zai iya gane saba noises da sautuna. A wannan yanayin, ne na al'ada martani ga bincike phonological audiogram.

Babban matsalar ta'allaka daidai a cikin filin na sauti ji na ƙwarai. Duk da wannan, da ciwo bayyana kanta a cikin mawuyacin lokaci na harshe saye na'urar. Sosai magana sake kunnawa iya zama daban-daban matakan mawuyaci. Aphasia ne sosai karfi a wasu marasa lafiya. Kamar yadda masana kimiyya ce, rikitarwa lokuta ana bincikar lafiya a 6 marasa lafiya daga 77. Idan yaro ya kiyaye qananan faru, shi za a iya ajiye karatu da rubutu basira. Harshe disturbances bayyana kamar haka: da yaro gauraya haruffa da kuma sauti daidai ba to gina sentences, ba zai iya Azancin ra'ayinsu da sauransu.

epilepsy

Clinical seizures an lura a 70-85% na lokuta na samu Landau-Kleffner ciwo. Rashin lafiya a wani uku na yara fara da guda farfadiya kãmun. Wannan shi ne - farkon da cutar. A yawan marasa lafiya tsakanin hari da kuma jawabin cuta iya daukar shekaru da dama. Seizures sukan gyarawa a shekaru 4 zuwa shekaru 10. Mutane da yawa likitoci sun ce ba su da faruwa a adult rayuwa. Wannan shi ne, bayan shekaru 16 na seizures ba faruwa.

A 58% na marasa lafiya da tsayayyen m seizures. Su haddasawa lalata da kwakwalwa Kwayoyin a wani takamaiman wuri na daya cerebral yammancin duniya. Seizures faruwa a 39% na yara, seizures tare da asarar sani - a 16%. Wasu marasa lafiya da fallasa myoclonic cuta ta shafi tsokoki na fuska da ido apples. A 12% da marasa lafiya epilepsy yana daukar kwayar cutar a cikin kwayoyin matakin.

halayya cuta

Su ne halayyar domin kusan dukan marasa lafiya. 78% na matasa da yara da halayya da matsaloli idan sun kamu da Landau-Kleffner ciwo. Manya Kada ka yi mamaki da cewa su sau daya cikin lumana da kuma m baby ba zato ba tsammani ya zama m. Rage - wani misali alama. Fushi iya zama haka m da kuma wanda ba a iya lura da shi ba, da cewa yaro ba zai iya iya jimre da shi ba tare da arin a wani tabin hankali ma'aikata. Others, a kan m, ya sami janye abruptly. Sun kauce wa kamfanin na mutanen da fama da tashin hankali da kuma m tunani.

Wasu yara ze zama gaba daya kurãme. Wasu sa ba daidai ba ganewar asali - Autism. Lalle ne, likitoci ne wani lokacin wuya a ƙayyade abin da real hanyar da m hali na wani Landau-Kleffner ciwo. Bayan duk, ya kuma autistic hali halin da mamaki kamar rashin iyawa to yi ma'ana cikawa na da tsari, da m maimaitawa na wannan phrases, kalmomi. Rauni maida hankali da hankali da kuma ya karu aiki lura a 80% da marasa lafiya. Ko da yake halin da matsaloli ne na biyu bayyanar cututtuka dangane da jawabin da matsaloli, wasu yara na iya mamaki sabon abu, illogical da m halayen. Alal misali, suna iya ciyar hours maimaita wannan karimcin.

zamani far

A farko alamar da cutar wajibi ne a fara jiyya na Landau-Kleffner ciwo. A asibitin, a cikin abin da za ka miƙa, za su iya bayar da wasu mafita ga matsalar:

• Drug hanya.
• tiyata.

A karshen harka, da mãsu haƙuri bude kwanyar da kuma cire farfadiya mayar da hankali. Don yin wannan, yanke wasu daga cikin ƙasusuwansa da kuma na da wuya harsashi na kwakwalwa. Bayan haka, da launin toka al'amari na Likita sa wani incision. Za su ci gaba da hana barkewar cutar da kuma yaduwar epileptogenic hatsaisai. Sai Dura Mathes da kasusuwa ne ya sa a wurin. The rauni ne sutured. Bayan 6-7 makonni bayan tiyata, da yaro daga asibiti iya komawa gida. Bayan tiyata a yara tare da Landau-Kleffner ciwo gani kyautata a cikin ilimi da kuma m ayyuka.

Anti-kãmun

Jiyya na Landau-Kleffner ciwo ne ba ko da yaushe bayar kawai sarrafawa bambanci. Wani lokaci yana taimaka wa rabu da cutar likita far. Yana bayar da liyafar na anticonvulsants. Abin baƙin ciki, ba su ko da yaushe ba wani sakamakon tabbatacce. Alal misali, "carbamazepine", "Phenobarbital", "Phenytoin" ne sau da yawa m - aphasia iya kawai samun muni. Seizures a marasa lafiya za a maimaita tare da ramuwa. Wannan Gaskiya ne, marasa lafiya da m seizures ko atypical rashi seizures.

Bugu da kari, sau da yawa likitoci bayar da shawarar "Nicardipine". Ya taimaka wajen toshe alli tashoshi. Amfani ne da gwamnatin igiyar jini gamma globulin. da kuma irin wannan sun tabbatar da isasshe tasiri miyagun ƙwayoyi "ethosuximide," "valproic acid". Taimako da kuma benzodiazepines, musamman "Clobazam" da "Midazolam". Amma su dole ne a gudanar intravenously.

wasu kwayoyi

Landau-Kleffner ciwo, cututtuka da jiyya da aka bayyana, a wannan labarin na samar domin liyafar na "Diazepam" kafin zuwa gado. Wannan magani bada sakamako mai kyau. Far an wajabta, a wani lokaci na 6 makonni don kauce wa tachyphylaxis - m rage sakamako tare da maimaita yin amfani da miyagun ƙwayoyi. Nazarin ya nuna cewa zai iya zama da amfani "levetiracetam". Haka kuma an sosai taimaka a lura da yara da idiopathic mai da hankali seizures, farfadiya lantarki matsayi na barci, danniya na ci gaba da karu tãguwar ruwa a cikin m lokaci. Bugu da kari, nasara da magani daga aphasia da seizures, da miyagun ƙwayoyi "felbamate." Amma lokacin da ka yi amfani da shi ne zai yiwu a ci gaba da dama illa, daga abin da ya fi akai-akai ci karo aplastic anemia da kuma hanta tabarbarewa.

corticosteroids

A lura da Landau-Kleffner ciwo da kuma taimako corticosteroids. "ACTH" musamman da kyau tabbatar. Ya rage bayyanuwar bayyanar cututtuka na samu farfadiya aphasia, daidai a cikin jihar daga cikin EEG. Dogon lokacin da far da wadannan kwayoyi ne shawarar mafi yawan marasa lafiya. Duk da haka, ka sani cewa ba kowa ne ya dace hormonal jiyya zaɓi.

Sau da yawa likitoci rubũta steroids ga marasa lafiya. Alal misali, "Prednisolone" da aka gudanar intravenously a watanni uku. A far da ake amfani da gafarar shigar da. Yana da muhimmanci a tuna cewa raguwa a sashi na steroids ne sau da yawa hade tare da m komawa cuta cututtuka. A total tsawon daga cikin shakka iya wuce daga watanni shida zuwa shekaru da dama. Ba zato ba tsammani, Corticosteroid magani yana da yawa illa kamar nauyi riba, hauhawar jini, da ciwon sukari, cataracts, koda gazawar, ciki, manic ciwo da sauransu. Bugu da kari, sun ba da shawarar ga marasa lafiya da suke da matsaloli tare da rigakafi, kamar yadda suka kara depress shi. Suna kuma contraindicated a cikin mutane tare da aseptic necrosis, da tarin fuka ko cututtuka wanda bayyanar tsokani m ayyuka na roundworms.

Da ra'ayoyi na iyaye

Special kula ake bukata domin yaro kamu da Landau-Kleffner ciwo. Sharhi kan iyaye nuna cewa wani jariri bukatar daukar azuzuwan ga wani jawabin ilimin, jawabin pathologists. Likita ba zai iya mayar da magana aiki. Amma wadannan zaman koyar da crumbs da juriyarsu, kawo a shi takalifi, kungiyar. Iyaye jayayya da cewa yara a kasashen waje don haka rubũta mai kyau anticonvulsant da antiepileptic magani da ake kira "Keppra". Mun kuma bayar da shawarar "Depakine," amma shi sau da yawa yana da wani mummunan tasiri a kan pancreas, don haka wasu sharuddan sauyawa zuwa homeopathic magani. Mutane da yawa iyaye mata da kuma kakanninsa sun kuma lura cewa hanya mafi kyau da ciwo - maturing baby. Ya samun mazan - An hankali inganta jawabin nasa. Bugu da kari, shekaru-gudu hare-hare da kuma paroxysms.

Outlook

Amma ga likitoci, suka kuma ci gaba da bincika abin da wani Landau-Kleffner ciwo. Photo marasa lafiya da su video aukuwa, tarihi, ya kammala kwararru kunkuntar profile - duk wannan wani bangare ne na bincike. Doctors lura da cewa far aiki mafi alhẽri a cikin taron cewa yaro halartar psychotherapy, jawabin azuzuwan. Cikakken dawo daga fi'ili ayyuka ne fairly rare. Yawancin lokaci 2/3 na yara ajiye fiye ko žasa tsanani magana Shingen.