Kiwon lafiya, Cututtuka da kuma Yanayi
Pancytopenia - a pathological yanayin a cikin abin da rage-rage a cikin zagawa da jinin dukan abubuwa na abun da ke ciki. Haddasawa, cututtuka, magani
Duk wani ci gaban da cuta a cikin jikin sa wani canji a yi daga gefe jini. Duk da haka, akwai wani yawan pathologies ga wanda irin wannan canje-canje ne babban asibiti fasalin. Pancytopenia - shi ne daya daga cikin pathological tafiyar matakai na hematopoietic tsarin, wanda aka bayyana a matsayin mai zaman kanta cuta, ko na iya zama wata alama wasu concomitant nosological.
Janar Concepts
Da cutar ba kowa, don haka mafi yawan mutane ba su sani irin wannan sabon abu. Pancytopenia - a Jihar rashi na da maikacin jini, da cin abin da aka sa ta munanan a cikin tsarin precursor jini Kwayoyin a mataki na hematopoiesis. Rage matakan ja da maikacin jini, da farin jini Kwayoyin da platelets saboda gaskiyar cewa kara Kwayoyin ba zai iya mayalwaci aiki.
Haka kuma cutar tasowa a biyu siffofin:
- idiopathic, ya sa ta ciki dalilai.
- sakandare, wanda aka sa ta waje tsoma.
A pathological yanayin a game da 50% na lokuta tasowa autoimmune irin. Wannan shi ne, jiki yana yaƙi kadai tare da maikacin jini, da mistaking su ga kasashen waje jamiái. Idiopathic form iya bayyana da aka makala na ƙarin waje factor cewa accelerates da m sakamako.
Pancytopenia - wata cuta da za a iya gaji, masu tasowa, a lokacin da jariri ne a cikin mahaifa. A yaro da aka haife riga da cuta daga jini-forming gabobin. Yana iya zama nakasar da kuma bargo hypoplasia, don haka da cewa tsarin ba zai iya jimre da ayyuka.
A etiology da cutar da kuma matsalolin na daban
Daga cikin babban Sanadin ci gaban da cuta ne kwayoyin maye gurbi, dogon lokacin da amfani da kwayoyi, rediyoaktif ko mai guba effects. Idiopathic nau'i ne halin da cewa a cikin hanyar ba za a iya kafa, duk da haka, akwai lokuta da cutar bayan haihuwa.
Tabbatar da dalilai, yana da muhimmanci ga wani m sakamako. Kawar da waje korau tasiri a wannan cuta - 50% nasara kudi.
Bugu da kari a cikin manyan dalilan akwai dalilai da dama da bayar da gudummawa ga ci gaban da Pathology:
- Aiki da benzene ko arsenic.
- Fanconi anemia.
- kwayar halitta daga kamuwa da cuta.
- jiyyar cutar sankara.
- maganin rigakafi da kuma immunosuppressants.
- autoimmune cututtuka irin na tsari lupus erythematosus.
- radiotherapy.
Fanconi anemia - daya daga cikin etiological dalilai na pancytopenia. Tasowa a kan bango na nakasar anomalies an dauki wani autosomal recessive cuta. Anemia ne halin gaban lahani a rabo na sunadaran alhakin DNA gyara da kuma chromosome friability.
The asibiti hoto da cutar
Pathological yanayin bayyana kanta a cikin nau'i na uku syndromes. Kowace daga cikin wadannan halayyar siffofin don rage yawan daya irin na jini Kwayoyin. Leukopenia aka nuna a hoto na m sepsis da zargin miki-necrotic matakai na fata da kuma mucous membranes.
Erythropenia da alama raguwa a haemoglobin tsokane da ci gaban da bayyanar cututtuka na anemia. Wannan jiha ne halin da:
- paleness na fata integument.
- tashiwa kafin idanunsa .
- dizziness.
- tinnitus.
- rauni da kuma gajiya.
- rauni.
Marasa lafiya koka shortness na numfashi da kuma zuciya palpitations. Auscultation domin sanin voiceless zuciya sautunan, systolic gunaguni a kan dukan surface na zuciya tsinkaya, amon saman lakar jannayẽnsa. Worsening da haƙuri da yanayin sa canje-canje a cikin electrocardiogram, wanda ya nuna ci gaban da zuciya rashin cin nasara.
Thrombocytopenia aka bayyana da m zub da jini (epistaxis, gastrointestinal, igiyar ciki), zub da jini gumis, bayyanar petechiae da hemorrhages a cikin fata. M bayyanar cututtuka da cutar ana sa ga game da wata, kuma sau da yawa kai ga mutuwa. Kullum pancytopenia yarda mafi m, kuma yana da wata kasa pronounced cututtuka
cutar da ake dauke su domin sosai hadaddun. Pancytopenia, wanda rikitarwa ne mafi kowa ga tsofaffi mutane, tare da bayyanar cututtuka da kuma zub da jini.
diagnostic matakan
A farko idan bukatar game da wani gwani dubawa, tarin tarihi da kuma rayuwar da haƙuri. Bugu da ari nada CBC. A cikin hali na wadannan Manuniya iya yin tunãni a kan ci gaban pancytopenia da kuma gudanar da bincike kara matakan:
- leukocytes <2 x 109 / l;
- platelets <150 x 109 / L;
- erythrocytes <3,5 x 109 / l.
Sanya nazari huda bargo, wanda ya kira gaban mahaukaci Kwayoyin da myelokaryocytes. Ƙaddara da gaban munanan, ciki har da bargo hypoplasia. Kuma gudanar da hemolytic samfurori.
pancytopenia magani
Warkewa matakai dogara ne a kan na asibiti hali, haƙuri da yanayin da etiological factor da ta haifar da cutar. Wadannan magani hanyoyin da za a iya amfani da:
- Jini, daidaita ma'auni na form abubuwa.
- Dasawa da bargo, ko kuma kara Kwayoyin. Sau da yawa marasa lafiya yi a cikin matasa da kuma magidanci.
- A cikin hali na autoimmune pancytopenia gudanar immunosuppressant aikace-aikace "Cytoxan", "Methylprednisolone," "Neoral", "Sandimun".
- Yana nufin stimulating da bargo aiki - "Neupogen", "Neulasta", "Procrit", "Leukin".
miyagun ƙwayoyi shuke-shuke
A hadaddun cuta far ya hada da yin amfani da ganye magani. A matakin na ja da maikacin jini, da haemoglobin za a iya tashe tare da taimakon berries. Garu teas aka sanya a kan tushen da ash, black currants, ya tashi kwatangwalo, strawberries, berries, apricot. Iron arziki kabeji da gooseberries, cherries da inabi, da cin abin da zai ba kawai daidaita ma'auni na da maikacin jini, amma kuma ƙarfafa tsarin na rigakafi.
A yawan jama'a hanyoyin domin zalunta pancytopenia qunshi zuma. An hade tare da wadannan kayayyakin:
- tare da ja ruwan inabi kuma Aloe.
- tafarnuwa.
- hatsi.
- lemun tsami, bushe apricots, zabibi, prunes da kuma walnuts.
Dora muhimmanci ga infusions da decoctions na magani ganye nettle nettle, Birch, ciyawa Sage, Clover, Dandelion, orchids, Clover, buckwheat.
ƙarshe
Pancytopenia - rashin lafiya mai tsanani, wanda daidaita zuwa m cuta. M sakamako dogara da tsanani daga asibiti ãyõyi, siffofin da kuma matakai na gaba a wadda magani fara. Irin wannan cuta ne sauki su hana fiye da zuwa magani.
A shekara-shekara likita jarrabawa na yawan taimaka wa ganewa na wani pathological yanayin a farkon matakai. A musamman wannan ya shafi dakin gwaje-gwaje jarrabawa hanyoyin.
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