Kiwon lafiyaMagani

Na huhu Vienna. Anomalous na huhu jijiyoyinmu

Na huhu Vienna (hoto da aka nuna a kasa) - wani jirgin ruwa da ya kawo jijiya jini da aka wadãtar da oxygen a cikin huhu zuwa hagu atrium.

An fara daga na huhu capillaries ci a cikin waɗannan kwanoni mafi jijiyoyinmu cewa an aika zuwa bronchi, sa'an nan segments kasarun adadi, da kuma huhu manyan kututturan ƙofar kafa (biyu daga kowane tushen) da cewa an fuskantar horizontally a cikin sama ɓangare na hagu atrium. Bugu da kari, kowacce daga cikin ganga shiga cikin wani raba bude: bar - a gefen hagu na bar atrium da dama daga dama. Dama na huhu veins, wadannan atrial (hagu) transversely rarraba dama atrium (ya mayar).

M huhu (dama) Vienna

Kafa segmental jannayẽnsa segments na tsakiya da kuma na sama huhu lobes.

  • R.apicalis (reshe apical) - wakilta short venous akwati, wanda aka located a kan babba lobe (mediastinal ta surface) da kuma daukawa jini daga kashi tip. Kafin shiga dama m huhu jannayẽnsa akai-akai a hade tare da segmental (raya) reshe.
  • R. na baya (raya reshe) daukawa jini tarin daga raya kashi. Wannan reshe - mafi daga dukan manyan Vienna jijiyoyinmu (segmental), wanda aka located in na sama lobe. A wannan jirgin ruwa ne ya zama ruwan dare da dama sassa: vnutrisegmentarny poddolevoy kashi da kashi cewa tattara jini daga interlobar surface yankin na QFontDatabase slits.
  • R.anterior (gaban reshe) daukawa jini daga cikin manya tattara rabo (ko agara kashi). A wasu lokuta, zai yiwu mu hada gaba da raya rassan (idan suka fada a cikin wani na kowa akwati).
  • R.lobi medii (tsakiya lobe reshe) na'am da jini daga hakkin huhu segments (ta talakawan rabo). A wasu lokuta, wannan daukan nau'i na daya Vienna ganga da gudana a cikin sama dama na huhu jijiya, amma sau da yawa matattarã aka kafa sassa biyu: da tsakiya kuma a kaikaice da lambatu daidai da tsakiya kuma da a kaikaice segments.

Lower na huhu (dama) Vienna

Wannan jirgin ruwa daukan da jini daga cikin ƙananan lobe (ta segments 5), kuma yana da biyu main inflow: muhimmi jijiya da kowa babba reshe.

A babba reshe

Shi ya ta'allaka ne tsakanin muhimmi da kuma na sama segments. An kafa daga ƙarin da kuma babban veins, ya zama a gaba da kuma saukar, wucewa a baya da apical segmental bronchus. Wannan reshe ne saman duk da cewa babu komai a cikin ƙananan dama na huhu jannayẽnsa.

Haka mashako Vienna qunshi uku main inflow: kaikaice, babba da tsakiya, located a mafi yawan intersegmental amma zai iya gudu kuma vnutrisegmentarno.

Saboda ƙarin jini outflow jannayẽnsa ɗauke da babba kashi (ta saman) a cikin yankin poddolevuyu segmental jannayẽnsa raya babba lobe (ta na baya sashi).

Basal total Vienna

Yana da wani gajeren venous akwati, kafa a jamsin na ƙananan kuma babba muhimmi jijiyoyinmu babban rassan da karya zurfi gaban kowa surface.

Basal saman Vienna. Kafa ta ci daga cikin mafi girma muhimmi segmental jijiyoyinmu da jijiyoyinmu da cewa kawo jini daga tsakiya, agara kuma a kaikaice segments.

Basal kasa Vienna. A haɗe da sauran muhimmi jijiya daga ta low baya surface. Babban inflow da ganga - muhimmi na baya reshe cewa tattara jini daga muhimmi na baya sashi. A wasu lokuta, da ƙananan muhimmi Vienna iya kusanci saman muhimmi jannayẽnsa.

ADLV

Yana da wani nakasar zuciya cuta a wadda aukuwa an gano neanatomichnoe na huhu jijiyoyinmu ga atrium (dama), ko hade a cikin latest na vena cava.

Wannan Pathology yana tare da m ciwon huhu, gajiya, shortness na numfashi, da bata lokaci ba na jiki ci gaba, cardiac zafi. Kamar yadda bincikowa da ake amfani da: ECG, MRI, X-haskoki, cardiac catheterization, duban dan tayi, kuma ventrikulo- atriografiyu, angiopulmonography.

M magani aibi dogara a kan ta irin.

Overview

ADLV - nakasar matsala kuma shi ne game da 1.5-3.0% na zuciya lahani. Mafi yawa daga cikin lura a namiji marasa lafiya.

Mafi sau da yawa wannan aibi ne a hade tare da wani m (bude) taga da lahani septum tsakanin ventricles. Dan kadan kasa (20%) - daga kowa akwati jini, hypoplastic gefen hagu na zuciya, VSD, dextrocardia, tetralogy na Fallot, kuma transposition daga cikin manyan tasoshin, janar zuciya ventricle.

Bugu da kari to waɗannan lahani, sau da yawa tare ADLV extracardiac Pathology: cibiyarki hernias, lahani a cikin kashi samuwar kuma endocrine tsarin, hanji diverticula, kofaton koda, polycystic koda cutar da kuma hydronephrosis.

Nau'in anomalous na huhu venous magudanun ruwa (ADLV)

A cikin hali na mahaɗar tsakãninsu da jijiyoyinmu a cikin tsari wurare dabam dabam, ko kuma a cikin dama atrium, wannan aibi da aka kira wani cikakken anomalous magudanun ruwa, idan a cikin sama tsarin gudana a cikin daya ko a 'yan veins, irin wannan aibi ne ake kira m.

A daidai da matakin na mahaɗar tsakãninsu ware wasu aibi zaɓuɓɓuka:

  • Da farko bambance-bambancen: nadserdechny (suprakardialny). A na huhu jijiyoyinmu (kamar kowa akwati ko raba) daga ƙarƙashinsu a cikin sama vena cava ko rassansa.
  • Option biyu: zuciya (intracardiac). Na huhu jijiyoyinmu drained cikin jijiyoyin zuciya sinus ko dama atrium.
  • Uku rungumi: podserdechny (infrared ko subcardial). Na huhu jijiyoyinmu shigar da portal ko vena cava ƙananan (da yawa kasa a lymphatic bututu).
  • A karo na hudu zaɓi: gauraye. Na huhu jijiyoyinmu kunshe a daban-daban Tsarin da a matakai daban-daban.

Features hemodynamics

A utero aiki aibi ne yawanci ba su gani ba, saboda peculiarities na fetal wurare dabam dabam. Bayan haihuwar jariri hemodynamic bayyananen ake tsare da wannan matsala kuma ta hade da sauran nakasar anomalies.

A cikin hali na jimlar anomalous magudanun ruwa na hemodynamic cuta bayyana hypoxemia, hyperkinetic obalodi na dama zuciya da kuma huhu hauhawar jini.

A cikin hali na m magudanun hemodynamics kama da cewa tare da ASD. Da rawar da haddasa nasa ne da keta mahaukaci arteriovenous shunt, wadda take kaiwa zuwa wani karuwa a jini girma a cikin wani karamin da'irar.

Alamun anomalous na huhu venous magudanun

Kids tare da wannan aibi sau da yawa sha maimaita m na numfashi kwayar cututtuka da kuma ciwon huhu, suka ce tari, low nauyi riba, tachycardia, shortness na numfashi, zuciya zafi, haske cyanosis da kuma gajiya.

A cikin hali na huhu hauhawar jini ne bayyanannu a cikin kananan shekaru bayyana zuciya rashin cin nasara, inda ya bayyana cyanosis da zuciya hump.

bincikowa da

Hoto auscultation a ADLV kama ASD, cewa shi ne fasali m auscultated systolic amo a cikin tsinkaya daga jijiyoyinmu arteries (na huhu jijiyoyinmu) da tsagawa da 2nd sautin.

  • A ECG ãyõyin dama zuciya obalodi, da karkacewa EOS dama kawancen (bai cika), dama dam reshe block.
  • Lokacin da phonography ãyõyin ASD.
  • A radiography samun juna haske bulging na huhu jijiya (ta baka), fadada dama cardiac iyaka, "Turkish saber" alama.
  • Echocardiography.
  • A gabansa cardiac cavities.
  • Venography.
  • Atriografiya (dama).
  • Angiography.
  • Ventriculography.

Bambanci ganewar asali na wannan aibi ya kamata a yi:

  • Lymphangiectasia.
  • Aortic atresia / mitral bawul.
  • tasoshin transposition.
  • Mitral stenosis.
  • Stenosis na da hakkin / bar huhu jijiyoyinmu.
  • Trehpredserdnym zuciya.
  • Ware ASD.

magani

Nau'in na tiyata m magudanun ƙaddara da daya lahani, size da wuri ASD.

Atrial sakon kashe ta amfani da roba ko suturing ASD. Jarirai har zuwa shekaru uku da suke cikin mawuyacin mawuyacin hali, gudanar da palliative tiyata (rufaffiyar atrioseptotomiyu), wanda aka nufin fadada interatrial sadarwa.

Total m aibi gyara (total siffofin) hada da dama jan.

  • Ligation pathological posts jijiyoyin bugun gini jijiyoyinmu.
  • Kadaici da na huhu jijiyoyinmu.
  • Ƙulli daga ASD.
  • Anastomosis tsakanin bar atrium da na huhu jijiyoyinmu.

A sakamakon irin wadannan ayyuka na iya zama: karuwa da na huhu hauhawar jini ciwo da kuma sinus kumburi gazawar.

kintace

A hangen nesa daga cikin halitta ba shakka wannan aibi ya fi karfinsu, tun 80% da marasa lafiya mutu a cikin shekarar farko ta rayuwa.

Marasa lafiya da gaban m magudanun iya rayuwa sama da shekaru talatin. Mutuwar irin marasa lafiya ne mafi sau da yawa dangantaka da na huhu cututtuka, ko mai tsanani zuciya rashin cin nasara.

Results daga m gyara daga cikin lahani sau da yawa m, amma a neonatal lethality a lokacin ko bayan tiyata ne high.

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