Mene ne Ollier cuta. Ollier ta cuta: bincike da kuma magance

Ka yi tunanin cewa ka kananan yaro kafafu ko makamai girma sannu a hankali? Zai yiwu ya Ollier cuta. Yana yake akwai wata cuta a cikin abin da akwai munanan daga kashi ci gaban da kwarangwal, cewa shi ne, ta dysplasia. Sauran sunayen da aka ambata cututtuka - mahara chondromatosis kasũsuwa, ashe, unilateral ko chondromatosis diskhondroplaziya ƙasũsuwa. Ya main suna cuta ya a madadin na Lyons likita Olier. A cuta ya gano da kuma bayyana ta hanyar amfani da X-haskoki a cikin 1899.

Menene cutar Ollier

Wannan cuta tana nufin munanan na fitar kasusuwan jikinsu kwarangwal, wanda nasa ne da yawa cututtuka, ciki har da sanannun mutane da yawa uwaye da yara hip dysplasia.

Cutar yawanci bayyana a cikin shimfiɗar jariri, saboda abin da aka a baya tunanin cewa wannan yara ta cutar. Yana yanzu ya tabbatar da cewa Pathology iya sa ya halarta a karon a manya (cututtuka na iya faruwa ko a cikin shekaru kewayon 20-40 years). Yana da wani nakasar abnormality, amma ta samu wasu lokaci daga baya - a farkon yara, ko a samartaka - wato, a lokacin da m girma, idan shi ya zama na fili nakasawa da ƙasũsuwa da / ko mahaukaci ci gaban da makamai da kuma kafafu.

Ollier ta cuta a cikin metaphyses na dogon tubular ƙasũsuwa da gabar jiki bayyana growths na guringuntsi. Cuta tasowa, yafi a kashi, guringuntsi, da kuma gidajen abinci na hannuwana da ƙafafuna, musamman a ƙafafunsa da hannuwansa, kazalika a ƙashin ƙugu, amma aka same shi a cikin hakarkarinsa, sternum, kuma kwanyar.

Growths ko enhondromy sa m Layer na kashi na bakin ciki da kuma gaggautsa. A gaskiya, shi ne mai kirki da ƙari da cewa zai iya ci gaba a cikin m (misali, chondrosarcoma). Abin farin, wannan ya faru sosai da wuya.

A lokacin balaga growths dattako da kuma maye gurbinsu da kashi.

Saboda haka, Ollier cuta - nauyi hereditary cuta, calcification na cartilaginous kwarangwal a wanda kuma ya auku da kuma thickening metaphyses (dogon ƙashi na daga wuyansa). Dalilin da ya faru shi ne har yanzu ba a sani ba. A wasu lokuta, shi ne wani autosomal rinjaye kwayoyin hali.

Similar to diskhondroplaziey cututtuka ne rare syndromes maffucci da Proteus. A farko, baya ga benign growths guringuntsi kuma kwarangwal musakai, fata kafa hemangioma - duhu ja spots sababbu siffar, kunsha na jini. A karo na biyu tasowa benign ciwace-ciwacen daji a sassa daban-daban na jiki.

Wanda aka shafi cutar

A baya can an yi tunanin cewa da ƙasũsuwa chondromatosis rare. Amma a yanzu, a lokacin da X-ray jarrabawa ne da za'ayi yadu isa, ya juya daga cewa shi ne, ba a rarity. Idan shekaru 20 da suka wuce, an bayyana 30 lokuta da cewa su ne yanzu sau biyu kamar yadda mutane da yawa.

Domin sanin ainihin farko yawanci ba zai yiwu ba idan a haihuwa bai kasance akai tsauri binciken yin amfani da X-haskoki, musamman a farkon lokacin kuruciya da kuma fetal ci gaba, a lokacin da, a gaskiya, babu Ollier cuta. A cuta ne, ta hanyar, da 'yan mata saukar kusan sau biyu mafi sau da yawa fiye da yara maza.

cututtuka

Ba miss da ãyõyin cuta, iyaye ya zama wary idan wani yaro:

• tsaya a gaban wasu sassa na wata gabar jiki / extremities.
• alama jeri na bangaren da kuma rage a gare su.
• ya lura lameness.
• akwai misalignment na kafafuwa.
• ba curvature daga cikin gidajen abinci na valgus ko cirewa zuwa tsakiya irin.

Duk wadannan abubuwan sa shi yiwuwa a ɗauka cewa yaro Ollier cuta.

Da cutar ba ko da yaushe nan da nan bayyananna a haihuwa, amma yana da shekaru 1-4 shekaru, za ka lura da cewa yaro ne a hankali fiye da sa ran, kara ƙafa ko hannuwa. Wannan shi ne babban alama da cutar, wanda ba za a iya watsi da. Sauran baby yana bunkasa kullum, duk da cewa ya kamu da "Ollier ta cutar."

Diskhondroplaziya mafi sau da yawa rinjayar daya reshe, duk da haka akwai lokuta da shan kashi biyu. Idan cutar ta shãfe saukar, yaron zai zama m girma saboda su rage. Musamman karfi da tsumburai ƙasũsuwa idan pathological aiwatar fara sosai farkon. Nakasawa ci gaba painfully jinkirin ci gaba. Hakika, daukan hotuna da cuta, ya zama guntu, thicker, canza Gait, lameness aka kiyaye. Akwai tsammãninsa ya zama tsakiya (varus), ko valgus deformity na gwiwa (m sau da yawa - da proximal ƙarshen femur ko kafar), scoliosis na kashin baya. Muscle atrophy a wannan cuta ba yanzu.

Big canje-canje ne batun a phalanx, yatsun kafa kuma, a wasu lokuta, da metacarpals. Su taqaitaccen, mika, m kuma guringuntsi dauke da yawa fadakarwa.

Ollier ta cutar na iya karaya a sakamakon cutar su ci gaba da ba daidai ba kashi. Duk da haka, sau da yawa samu karaya seamlessly overgrown.

Comorbidities

Diskhondroplaziyu iya bi raunuka na sauran gabobin, ko da yake related cututtuka ci gaba ne ba ko da yaushe. A musamman, a cikin 'yan mata matasa tare da Ollier ta cutar na iya faruwa teratoma na kwai da kuma endocrine cuta, ciki har da mai tsanani, ciki har da sosai farkon haila kuma precocious mafarki kara ossification.

Duk da haka, ci gaban da aka mayar da su zuwa al'ada ta cire wani kwai ƙari.

bincikowa da

Don gane Ollier ta cuta, shi ne na farko dole ya yi roentgen. Akwai kamata kuma ya kasance wani kashi biopsy da Magnetic rawa Dabarar. Bayan ganewa na cuta, marasa lafiya bukatar yau da kullum rajistan shiga-rubucen da wani likita, idan ya cancanta, to da sauri gane m canji zuwa chondrosarcoma.

bambanci ganewar asali

Bambanci ganewar asali Ollier ta cuta, a gaskiya, ba dole bayan da X-ray, saboda hoto ne sosai musamman chondromatosis. Duk da haka, kowane hali ne mutum ba, amma wani sa na m bayyanar cututtuka kusan maimaita, don haka likitoci dole ne sarauta daga wani adadin kama cututtuka.

Roentgen gusar atypical Chondrodystrophy, hemihypertrophy ko kashi atrophy, rachitic nakasawa da kuma wasu sauran cututtuka. Har ila yau, saboda X-haskoki, shi ne cire Recklinghausen cuta, wanda yawanci za a iya rikita Ollier cuta. Babban manufa - za mu yi wani x-ray dukan kwarangwal, maimakon ɓangare na shi.

magani Jagororin

Diskhondroplaziya a wannan lokacin, da rashin alheri, yana da wani m hanyoyin magani. A bambanci, misali, irin cututtuka kamar hip dysplasia, chondromatosis bi da kawai da m gyara na nakasawa. A wasu lokuta, shi nuna wani wucin gadi hip sauyawa. Sauran magani da mãsu haƙuri ya kamata sami, - symptomatic da kuma taimaka.

M baki yana nuna yafi ga manya, tun da, a cewar zamani lura, a lokacin da m gyara a makaranta shekaru m sakamakon da aka samu, wanda ke nufin cewa abin nufi da m magani ne kawai a kafa a lokacin nakasawa, amma ba tsauri. Duk da haka, a cikin tsanani raunin yiwu tiyata ga yara, musamman a lokacin da ya zo ga yatsunsu, wanda ake muhimmanci gurbata a Ollier cuta.

Cutar na bukatar rike hadin gwiwa da kuma kashi: marasa lafiya nuna saka orthopedic takalma, da yin amfani da orthopedic Katakon da kuma wasu na'urorin don kayyade gidajen abinci. Marasa lafiya dole ne tafiyar tsara musamman domin wannan Pathology magani da kuma motsa jiki wasanni hadaddun.

Amfani kamar yadda gymnastics da kuma darussan kan musamman simulators. Ya taimaka wajen mayar da tsoka sautin da karfafa jijiyoyin.

Outlook

Kamar yadda bincike, mafi sau da yawa a cikin mafarki, guringuntsi aka maye gurbinsu da kashi (watakila shi ke sa a adult lokuta da cutar suna gano sosai da wuya). Duk da haka, da aka yi hasashen ne kasa da raduzhen a matasa da yara: nakasawa, albeit sannu a hankali, amma an ci gaba. Wannan shi ne abin da yake da ha ari Ollier cuta.

Haka kuma cutar bayyana kanta don haka akayi daban-daban a cikin kowane hali, da cewa overall hangen nesa da wuya a tantance ainihin. Lokacin da mahara raunuka shi ne mafi m fiye da a cikin hali na guda sarrafa gyara. Single nakasawa take kaiwa zuwa wani rage na daya daga cikin wata gabar jiki da kuma inganta, da su jeri na bangaren, musamman a lokacin da ta je kananan yara. Kuma ba shi yiwuwa a kafa. Har ila yau, a cikin farkon cin gaban ciwon daji na kara hadarin daban-daban nakasar da yatsunsu.

Canji a cikin chondrosarcoma

Duk da cewa m canji a view - chondrosarcoma - ba ya faru sau da yawa, duk da haka akwai damar bunkasa ciwon daji. Mafi yawa wannan ya faru a cikin samartaka, ko da yake wani adadin na yanzu bincike ya nuna cewa shi zai iya faruwa da yawa daga baya. Saboda wannan dalili, marasa lafiya suna shawarar diskhondroplaziey yau da kullum da shawarwari tare da wani likita da likita Nazarin.