Kiwon lafiya, Cututtuka da kuma Yanayi
Darier ta cuta: haddasawa, cututtuka, magani
Mafi yawa daga cikin mutane shi ne ainihin replica iyayensu. Daya samun blue idanu na shugaban Kirista, da sauran - chic mahaifiyarsa ta gashi. Hakika, wani lokacin sabanin haka ba. Duk da haka, mu duka girma ban sha'awa sakamakon saƙa genes na mu kusantar dangi. Sau da yawa sosai, tare da manyan idanu, curly gashi kuma dogon kafafu, iyaye ba su yara a sa na daban-daban cututtuka. Sun yi wannan ba a kan manufa, ko da ba tare da naka yarda. Pathology iya faruwa ba cikin rayuwa, amma mafi sau da yawa yanayin da ake ciki ne daban-daban. A mutum ya zama mai yi garkuwa da iyali cututtuka da kuma ailments. Daya daga cikin wadannan "kyautai" ne Darier cuta. Mene ne wannan? Abin da ya haddasa wannan Pathology?
janar bayanai
Karkashin Darier ta cutar tana nufin wani hereditary dermatosis bayyana rash a cikin nau'i na nodules ruwan kasa ko ruwan kasa. Su mazugi-dimbin yawa, kuma an rufe shi da lokacin farin ciki crusts. Nodules sarrafa a jiki folds zo tare da kuma samar da wani m rauni. Ya danganta da wurin da raunuka da kuma su bayyanar, Darier ta cuta ne zuwa kashi hudu siffofin:
- Sarrafa. Halin da a mikakke tsari daga cikin cibiyoyin da wanda rufe kawai iyakance yankunan na jiki.
- Gargajiya. Rash yawanci sarrafa a kan fatar kan mutum, kirji da kuma kunnuwa.
- Ware. Tare da misali nodules bayyana polyhedral papules kama warts. Yawanci, suna a kan mayar da hannuwansa da ƙafafunsa.
- Vesicular-bullous. Wannan nau'i na cutar ne sosai rare. An halin mahara raunuka tare da m m. Sun bayyana a gefen wuyansa, a yankin na manyan fata folds.
Primary raunuka papules ake bincikar lafiya a marasa lafiya dake da shekaru takwas zuwa goma sha biyar shekaru. Adult rashin lafiya buga wuya.
A Sanadin cutar
Babban dalilin wannan cuta ne gaban mahaukaci gene, da kuma wata babbar hadarin factor - gaji predisposition. A sakamakon haka, bitamin A da aka ba da cikakken samamme ta jiki, da ayyukan wasu enzymes da kuma tutiya abun ciki a cikin epidermis an rage. A sakamakon wadannan pathological tafiyar matakai a take ginshikai na fata keratinization.
Idan inna ko baba ne dako na mahaukaci gene a 50% na lokuta, haske ya bayyana yaro da ganewar asali "Darier ta cutar." Duk da haka, idan marasa lafiya iyaye haife cikakken lafiya baby, wannan Pathology ba dame ya nan gaba 'ya'yanku. Da cutar ba a daukar kwayar cutar ta hanyar Airborne droplets ko jima'i.
asibiti hoto
A pathological aiwatar fara da bayyanar lebur follicular nodules, wanda ake in ba haka ba da aka sani da papules. Su size iya bambanta daga 1 zuwa 3 mm. Papules rufe tare da m ɓawon burodi na ruwan kasa launi. Karkashin shi akwai depressions a cikin siffar wani mazurari. Nodules suna located a bakin gashi follicles, wanda wani lokacin take kaiwa zuwa cin gaban wani cuta - folliculitis. Saboda haka, kafin fara jiyya wajibi ne a gudanar da wani bambanci ganewar asali.
Eruptions aka shirya symmetrically grabbing subclavian yankin da kuma flexor saman na gidajen abinci. A fatar kan mutum papule reminiscent warty scaly plaques da crusts. Bayan su kau, a wurare da raunuka bayyana foci na alopecia. Kamar yadda cutar progresses akwai sabon rashes da kuma tsohon ci a cikin guda tabo.
Medical jarrabawa
Ganewar asali da cutar dogara ne a kan na asibiti hoto da kuma cikakken likita tarihi na haƙuri. A lokacin jarrabawa, likita na nazarin cututtuka na cuta, baya lokuta na rashes tsakanin kusantar dangi. Don tabbatar da cutar da aka sanya a histological bincike na fata biopsy. A bambanci ganewar asali ne da za'ayi tare da iyalinmu pemphigus, papillomatosis da seborrheic dermatitis.
far ka'idodin
Jiyya tare da wannan rashin lafiya ya saba yi a kan wani outpatient akai. A lokacin exacerbation na pathological aiwatar bayyana ko m raunuka haƙuri bukatar arin a dermatological asibiti.
A haƙuri ne symptomatic far. All marasa lafiya da ba togiya sanya bitamin A, a cikin nau'i na baka ko intramuscular allura. Sashi da aka lasafta akayi daban-daban, shan la'akari da haƙuri da shekaru. A hanya na lura shi ne yawanci 3 months, sa'an nan yin hutu da kuma maimaita jiyya.
A sakamakon tabbatacce tare da Darier cuta ba kumfa baho a hade tare da aikace-aikace keratolytic maganin shafawa. A gaban manyan raunuka, m baki ko electrocoagulation. Lokacin da Darier ta cuta yana tare da Bugu da kari na wani kwayan kamuwa da cuta, wani kwayoyin da aka wajabta.
Hasashen da kuma rigakafin
Cutar da ake daukar kwayar cutar na musamman ta hanyar gado. Wannan shi ne dalilin da ya sa a matsayin na farko rigakafin masana bayar da shawarar shawara da jini ga ma'aurata shirin a kusa lokaci conceiving yaro. Wannan Gaskiya ne, daga cikin iyaye, wanda a cikin iyali, an riga an kamu da Darier ta cutar.
A magani aka bayyana a sama, yawanci nuna sakamako mai kyau. Mutane da yawa marasa lafiya za su iya cimma gafarar dage domin 'yan shekaru. Duk da haka, wanda ya kamata ba zata cikakken maida.
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