Abin Pathology kira Weber ciwo? Weber ciwo: haddasawa, cututtuka da kuma magani

Sturge-Weber ciwo - wani gaji cuta na zuwa rukuni na alternating hemiplegia. Yana hadawa da shan kashi na girman jijiyoyi daga hearth da cuta azanci da kuma mota ayyuka a gefen. Weber ciwo kira neurological ciwo, a cikin abin da kashin baya, ko lalace tsakiya na oculomotor jijiya. Hankula bayyanar cututtuka da cutar suna gane a kan fuskarsa, a gefe na hearth akwai ptosis, mydriasis, strabismus, tsakiyar contralateral hemiplegia, inna na tsokoki na fuska da kuma harshe.

Weber ciwo: ãyõyinSa

Weber ciwo yake akwai wata cuta a cikin abin da ya bayyana a cikin shafi yankunan da fata angiomas, angioma kuma lura da ido tasoshin conjunctiva. zai yiwu ci gaban cataracts, glaucoma, kuma retinal detachment.

kafa mahara angioma, wanda kuma ya shafi fata da kuma kewaye kyallen takarda, bayyana halayyar neurological cututtuka a Pia Mathes. Mafi sau da yawa cutar rinjayar da wuri daga cikin manya muƙamuƙi da ido trigeminal jijiya. Lalacewar kwakwalwa taushi harsashi iya zama ko dai kawai daya gefen, ko shafi duka.

The shafa yankin na fuska ta rufe musamman faci na ja launi, da, ban da juyayi tsarin, cutar na iya shafar ciki gabobin.

Weber ciwo ne halin da wadannan cututtuka:

• A hotuna MRI ko CT duba - nuni leptomeningeal angioma.
• Convulsive dauki.
• Shafi tunanin mutum retardation (idiocy, shafi tunanin mutum retardation).
• Karuwan intraocular matsa lamba.
• Rashi na view.
• Hemiparesis.
• Atrophy.
• Angiomas (ja fata ta rufe tare da jijiyoyin bugun gini faci).

Weber ciwo jinsunan

Gane dama manyan iri. Aka bayyana a sama ya nuna da cutar - Weber ciwo. Photo nuna look daga wani mutum fama da wannan cuta. Cutar da ake rarraba su zuwa:

• Schirmer-ciwo - farkon cin gaban glaucoma da ocular manifestations cutaneous angioma.
• Milles-ciwo - hemangioma ido ci gaba ba tare da shiga tare da farkon glaucoma cututtuka angiomas a kan fata da idanu.
• Knud-Rrubbe-ciwo - wata alama ce ta angioma entsefalotrigeminalnoy.
• Weber- Dumitri-ciwo - wata alama ce ta epilepsy, seizures, na cin gaba da bata lokaci ba, hemihypertrophy.
• Jahnke-ciwo - angioma na fata, yankunan da kwakwalwa.
• Loford-ciwo - angioma eyeball ba tare da magnification.

Weber ciwo: Sanadin

A sabili da cutar ta'allaka ne da cewa, a lokacin da ci gaban da tayin lalace biyu jam yadudduka: ectoderm da kuma mesodam. A ci gaba da yara da wannan cuta ne sosai harben. The rashin lafiya yana daukar kwayar cutar da farko ta rinjaye alleles, amma da ta faru da kuma recessive gādo.

Da cutar zai iya ci gaba a tayin da hali na ciki yana da wani mummunan tasiri. Wadannan sun hada da:

• Smoking a lokacin daukar ciki, musamman a farkon matakai.
• A amfani da barasa.
• Yi amfani da kwayoyi.
• Maye daga cikin mata masu ciki da daban-daban etiologies.
• A uncontrolled amfani da kwayoyi.
• Al'aura cututtuka samu a lokacin daukar ciki.
• Intrauterine kamuwa da cuta.
• Cuta a cikin expectant uwa metabolism (hypothyroidism).

Sau da yawa, wajen samar da cutar kawai rinjayar gadar hali. Weber ciwo ba za a iya kamuwa da a rayuwar yau da kullum.

ganewar asali da cutar

Cutar da ake kamu da halayyar manifestations. Sashe na daga cikin haƙuri ta fuska aka fallasa angiomatous canje-canje, ta ƙara ido matsa lamba tare da wani yiwu karuwa daga cikin eyeball, suna da farfadiya seizures. Idan akwai tuhuma da Weber ciwo, bincike da kuma magance suna da za'ayi da dama likitoci: ophthalmologist, neurologist, epileptologist, likitan fata.

Don fayyace wannan ganewar asali na bukatar X-ray jarrabawa. A kan samu na hotuna za a iya gani calcification na cerebral bawo. Lissafta tomography samar da wani ko da more cikakken hoto na shafa yankunan. Hotunan kama da MRI, za a iya gane thinning na cerebral bawo, degeneration da atrophy na fari al'amarin. Hardware bincikowa kamata kuma ya kasance kebe da sauran, daidai hatsari cututtuka: kwakwalwa ƙari, ƙurji taushi kwakwalwa nama cysts.

A babbar rawar ga daidai ganewar asali taka EEG gudanar, tun da shi ya sa ya yiwu don ƙayyade da ayyukan bioelectric hasken dake fitowa a cikin kwakwalwa, a lokacin da za a gane asali epilepsy. Mafi yawan mutanen da ke fama daga ciwo na Weber, suna da farfadiya seizures. Har ila yau gudanar ji na intraocular matsa lamba, filin ra'ayi, ophthalmoscopy, AV scanning - to nada ophthalmic magani.

Weber Syndrome Jiyya

Weber ciwo a halin yanzu wani tasiri magani ba za'ayi da kuma magani ne da nufin alama taimako da kuma inganta ingancin rayuwa. A haƙuri da ake sa anticonvulsant far da daban-daban magunguna:

• "Depakine."
• "Carbamazepine."
• "Keppra".
• "Topiramate".
• "Finlepsin".

Popular sau da yawa da haƙuri ba ya amsa da magani daga farfadiya seizures, sa'an nan likita iya nada a matsayin yin amfani da mahara kwayoyi. Idan ba ka taimake usilenaaya far, da shaidar da wani neurosurgeon iya sanya wa m magani.

Dagagge intraocular matsa lamba (glaucoma) yana bi da musamman saukad, rage mugunya ruwa-ruwa mutumci. Wadannan kwayoyi hada da "timolol", "Alfagan", "Azopt," "Dorzolamide". Duk da haka, wannan ra'ayin mazan jiya far iya zama sosai wanda ya kasa aiki, sa'an nan kadai zaɓi ne tiyata: marasa lafiya underwent trabeculectomy ko trabekulotomiyu.

Sakamakon da rikitarwa

Weber Syndrome - ne mai hadarin gaske cuta. A cikin hali na ra'ayin mazan jiya, ko m magani da aka hadu da haƙuri da yanayin da ya ba inganta, ba a wajen talakawa hangen nesa. Uncontrolled farfadiya ciwo zai iya kai wa ga gigin-tsufa, shafi tunanin mutum retardation, makanta, ya karu hadarin bugun jini.

Rigakafin cutar

Duk da cewa cutar ne hereditary, m matakan da za'ayi da mace mai ciki, zai rage hadarin bunkasa cutar. Wadannan ayyuka sun hada da:

• Ƙin na miyagun halaye (musamman a lokacin daukar ciki).
• Kasancewa daidai da lafiya salon. M tafiya a cikin sabo ne iska, da lafiya barci.
• Proper tsaga abinci. An karuwa a rage cin abinci tare da high fiber abinci. Kada ka yi amfani da Semi-ƙãre kayayyakin da soyayyen abinci.
• Dace rajista tare da juna biyu da kuma ziyara ga likita a shirya lokaci.
• Da amfani da kwayoyi kawai domin ta yi nufin sayen magani.

Weber ciwo - a rare kuma m cuta, wadda ana kai tsaye nuna a kan ingancin rayuwar dan Adam. Trust likitoci, dace ganewar asali da kuma nassi na wajabta magani iya canja rayuka da mafi alhẽri. Yana da muhimmanci kada su bari cutar da dauki hanya, kuma ba su yi amfani da kwayoyi ba tare da takardar sayen magani.